An Unusual Cardiac Anomaly: Ebstein-like Malformation
نویسندگان
چکیده
E BSTEIN’S ANOMALY, FIRST DESCRIBED in 1866, is relatively rare. It is a downward displacement of the tricuspid (right atrioventricular) valve below its annulus, dividing the right heart into a relatively large atrium and a small, at times functionless, right ventricle. The foramen ovale is usually patent and there may be other intracardiac anomalies.” We are describing a similar lesion involving the left atrioventricular valve, seen in an adult who seemed to have dextrocardia.
منابع مشابه
Bilateral Ebstein-like anomaly with atrial septal defect.
We report an unusual congenital cardiac anomaly consisting of a downward displacement of all leaflets of both atrio-ventricular valves. In addition to these changes, an atrial septal defect of the secundum type was noted. In light of the extreme rarity of this interesting anomaly complex, we reviewed the literature and compare the morphologic features of the present case with classic Ebstein's ...
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